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Pulmonary capillaritis leading to alveolar hemorrhage in a juvenile idiopathic arthritis patient: first description

Identifieur interne : 001518 ( Main/Exploration ); précédent : 001517; suivant : 001519

Pulmonary capillaritis leading to alveolar hemorrhage in a juvenile idiopathic arthritis patient: first description

Auteurs : Elisa Watanabe [Brésil] ; Leonardo Rios Diniz [Brésil] ; Licia Maria Henrique Da Mota [Brésil] ; Solange Murta Barros [Brésil] ; Jozélio Freire De Carvalho [Brésil]

Source :

RBID : ISTEX:67A6769B13E55082B90494022368D6ACB0708017

English descriptors

Abstract

Abstract: Juvenile idiopathic arthritis (JIA) is characterized by the typical joint involvement and some patients have extra-articular lesions, such as uveitis and pleuritis. However, until this date, no case of alveolar hemorrhage in JIA has been described. Herein, the authors describe a case of a male patient, 33 years old diagnosed as polyarticular JIA who had a dramatic evolution with alveolar hemorrhage secondary to pulmonary capillaritis. He received intravenous immunoglobulin and pulse therapies with glucocorticoid and cyclophosphamide with a satisfactory outcome. In addition, the authors review this important pulmonary complication in rheumatic diseases.

Url:
DOI: 10.1007/s00296-011-2035-3


Affiliations:


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